Archives of the Turkish Society of Cardiology
Biventricular noncompaction cardiomyopathy with severe systolic and diastolic dysfunction in a systemic sclerosis patient [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2015; 43(8): 720-723 | DOI: 10.5543/tkda.2015.62392

Biventricular noncompaction cardiomyopathy with severe systolic and diastolic dysfunction in a systemic sclerosis patient

Belma Kalaycı1, Süleyman Kalaycı2, Turgut Karabağ1, Mustafa Aydın1
1Department of Cardiology, Bülent Ecevit University Faculty of Medicine, Zonguldak, Turkey
2Department of Cardiology, Zonguldak Atatürk State Hospital, Zonguldak, Turkey

Non-compaction cardiomyopathy (NCM) is a rare congenital cardiomyopathy characterized by deep increased trabeculation in one or more segments of the ventricle. The apical segment of the left ventricle is most commonly affected, but left ventricular basal segment, biventricular involvement or right ventricle predominance have also been described. While some neuromuscular anomalies and myopathies had been described in systemic sclerosis patients, coexistence of chronic inflammatory disorders and NCM is unclear. This paper presents a case of biventricular NCM with severe systolic and diastolic dysfunction in a 40-year-old female diffuse cutaneous systemic sclerosis patient.

Keywords: Non-compaction cardiomyopathy, systemic sclerosis









How to cite this article
Belma Kalaycı, Süleyman Kalaycı, Turgut Karabağ, Mustafa Aydın. Biventricular noncompaction cardiomyopathy with severe systolic and diastolic dysfunction in a systemic sclerosis patient. Turk Kardiyol Dern Ars. 2015; 43(8): 720-723

Corresponding Author: Belma Kalaycı, Türkiye
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