ISSN 1016-5169 | E-ISSN 1308-4488
Archives of the Turkish Society of Cardiology
Incidence of İdiopathic Long QT Syndrome in Children With Congenital Deafness [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 1996; 24(1): 26-30

Incidence of İdiopathic Long QT Syndrome in Children With Congenital Deafness

Burhan ÖCAL1, Ayten İMAMOĞLU1, Semra ATALAY1, Muharrem GÜLDAL1

Long QT syndrome is characterized by a prolongation in the QT interval, associated with a high risk for syncope and sudden death. Jervell and Lange-Nielsen had initially deseribed it in association with congenital deafness. We have investigated the incidence of this syndrome in a school for deaf children; 350 children w ith an age range of 6-19 were evaluated by ECG. Corrected QT interval was calculated by Bazett's formula. Eight children with a QTc interval greater than 0.44 see were further studied: Cardiac examination, repeated ECGs (3 times), Rolter monitoring, echocardiography and exercise tests were performed for these 8 children. The families were assessed in regard to a history of syncope and deafness, as well as a lengthened QTc interval. Two girls, aged 14 and 15, were diagnosed to have long QT syndrome according to Schwartz criteria (0.57 % among the 350 children). The first case had two major (QTc=483 see and history of syncopal attack) plus one minor criteria (congenital deafness), the second girl had two major (QTc= 613 see and family members with LQTS) plus one minor criteria (congenital deafness). Prophylactic beta bloeker therapy was started. This syndrome should be sought for in children with syncope or a family history of it, especially in children w ith loss of hearing.


How to cite this article
Burhan ÖCAL, Ayten İMAMOĞLU, Semra ATALAY, Muharrem GÜLDAL. Incidence of İdiopathic Long QT Syndrome in Children With Congenital Deafness. Turk Kardiyol Dern Ars. 1996; 24(1): 26-30
Manuscript Language: Turkish


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