A Case with Paget Shrotter Syndrome: A Rare Primary Upper Vein Thrombosis

Thrombosis of deep veins of the upper extremity (UEDVT) is quite rare, accounting for only 1-2% of deep ve in thrombosis in the body. Primary UEDVT is a rare disorder that refers either to effort thrombosis or idiopathic UEDVT. Paget-Schrotter syndrome, effort thrombosis, was initially deseribed in 1875 in the patients w ith spontaneous UEDVT, usually intheir dominant arnı, after a strenous activity. The heavy exertion causes microtrauma to the vessel intima and leads to activation of the coagulation cascade. Anticoagulation, the comerstane of the therapy, helps to maintain patency of venous collaterals and reduces thrombus propagation. In this paper, we present a patient with well-developed collaterals, and could be treated w ith warfarin successfully. Paget-Schrotter syndrome should be considered in the dif.ferential diagnosis in a young patient admitted with pain and swelling of dominant upper extrenıity. Although the patient, presented in this paper, was treated with anticoagulation successfully, to prevent the complications such as post-thronıbotic syndrome that nıay affect the health quality of these young patients, more aggressive treatnıents, such as thronıbolysis, should be considered.