ISSN 1016-5169 | E-ISSN 1308-4488
Archives of the Turkish Society of Cardiology
Combination of complete atrioventricular septal defect and tetralogy of Fallot: surgical management and its results [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2008; 36(7): 461-466

Combination of complete atrioventricular septal defect and tetralogy of Fallot: surgical management and its results

Tayyar Sarıoğlu1, Ersin Erek1, Yusuf Kenan Yalçınbaş1, Yasemin Türekul1, Arda Saygılı2, Ayşe Sarıoğlu2, Ayşe Ulukol3
1Acibadem Bakirkoy Hospital, Cardiovascular Surgery Department, Istanbul, Turkey
2Acibadem Bakirkoy Hospital, Pediatric Cardiology, Istanbul, Turkey
3Acibadem Bakirkoy Hospital, Anesthesiology And Reanimation, Istanbul, Turkey


OBJECTIVES
Complete atrioventricular septal defect (AVSD) with tetralogy of Fallot (TOF) is a rare congenital heart anomaly. We evaluated surgical results of total repair in patients with TOF and AVSD.

STUDY DESIGN
Seven patients (5 girls, 2 boys; age range 2.5 to 14 years) underwent total repair for AVSD and TOF. Three patients had Down syndrome. Three patients had previous systemic-to-pulmonary shunt operations. Accompanying anomalies were left superior vena cava (n=2), left atrial isomerism (n=1), muscular VSD (n=1), and double outlet right ventricle (n=1). Preoperative diagnoses were based on echocardiographic examinations. The two-patch technique was used for surgical repair. Reconstruction of the right ventricular outflow tract was performed using transannular and infundibular patches in four and three patients, respectively. The follow-up period ranged from six months to nine years (mean 3.4±2.9 years).

RESULTS
No mortality occurred throughout the follow-up period. Two patients had prolonged hospitalization (>1 month) due to pulmonary infection and sepsis. At the latest follow-up, functional capacity was NYHA class I in five patients, and class II in two patients. Final echocardiographic examinations showed mild left atrioventricular (AV) valve insufficiency in five patients, and mild (n=3) or moderate (n=1) right AV valve insufficiency. Two patients had mild residual pulmonary stenosis, and three patients with a transannular patch had free pulmonary insufficiency. All the patients had proper right and left ventricular functions and all were in sinus rhythm.

CONCLUSION
With a proper surgical strategy and technique, AVSD and TOF can be corrected successfully. Long-term follow-up is necessary for AV valve dysfunction and pulmonary insufficiency.

Keywords: Child, heart defects, congenital; heart septal defects, atrial/surgery; heart septal defects, ventricular/surgery; pulmonary artery/surgery; tetralogy of Fallot/surgery

How to cite this article
Tayyar Sarıoğlu, Ersin Erek, Yusuf Kenan Yalçınbaş, Yasemin Türekul, Arda Saygılı, Ayşe Sarıoğlu, Ayşe Ulukol. Combination of complete atrioventricular septal defect and tetralogy of Fallot: surgical management and its results. Turk Kardiyol Dern Ars. 2008; 36(7): 461-466

Corresponding Author: Ersin Erek, Türkiye
Manuscript Language: Turkish


Journal Metrics

Journal Citation Indicator: 0.18
CiteScore: 1.1
Source Normalized Impact
per Paper:
0.22
SCImago Journal Rank: 0.348

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