A case of cor triatriatum diagnosed by echocardiography

Cor triatriatum is a rare congenital cardiac anomaly in which the left atrium is divided into two compartments by an abnormal fibromuscular septum, resulting in varying degrees of obstruction of the pulmonary venous return and causing pulmonary venous and pulmonary arterial hypertension. Echocardiographic examination showed cor triatriatum in a six-month-old female infant who had frequently recurring lung infections and immune deficiency. She was submitted to surgery where the diagnosis was confirmed by cardiac catheterization and angiography. Since open surgical correction, she has been under follow-up for six months without any complications.