Noncompaction of the Myocardium, A Rare Cardiomyopathy: A case report [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2001; 29(5): 321-324

Noncompaction of the Myocardium, A Rare Cardiomyopathy: A case report

Yüksel ÇAVUŞOĞLU1, Necmi ATA1, Bilgin TİMURALP1, Bülent GÖRENEK1, Ömer GÖKTEKİN1, Gulmira KUDAİBERDİEVA1, Ahmet ÜNALIR1

Noncompaction of the myoc ardiuın (NM) is a rare cardiomyopathy due to an arrest of in trauterine ın yocardial morphogenesis. The c haracteris tic echocardiographic findings are multiple, proıninent myocardial trabeculations and deep intertrabecular recesses. The clinic manifestations ineJude heart failure, arrhythmias and embolic events. It has been deseribed in association with presence of some genetic abnorınal ities . We deseribe a case of NM with bicuspid aorta in a 19-year-old male with typical elinical and echocardiographic fea tures of the disease. Clinically, the patient had s igns of progressive worsening of heart failure. ECG demostrated left anterior hemiblock. Cardiomegaly was found in teleradiography. Echocardiography revealed a markedly dilated left ventricle with severely impaired systolic function (ejection fraction; 0.27), characteristic, multiple, prominent trabeculations in the left ventricular apex, bicuspid aorta and moderate degrees of aortic regurgitation. Despite aggressive medical treatment, patient died on the 14th day of hospitalization. This is the first reported case of NM in Turkey, and it is considered as cardiomyopathy.

Keywords: Noncompaction of the myocardium, cardiomyopathy, bicuspid aorta.

How to cite this article
Yüksel ÇAVUŞOĞLU, Necmi ATA, Bilgin TİMURALP, Bülent GÖRENEK, Ömer GÖKTEKİN, Gulmira KUDAİBERDİEVA, Ahmet ÜNALIR. Noncompaction of the Myocardium, A Rare Cardiomyopathy: A case report. Turk Kardiyol Dern Ars. 2001; 29(5): 321-324
© Copyright 2019 Archives of the Turkish Society of Cardiology
LookUs & Online Makale