ISSN 1016-5169 | E-ISSN 1308-4488
Archives of the Turkish Society of Cardiology
Pediatric pulmonary hypertension [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2014; 42(1): 153-164

Pediatric pulmonary hypertension

D. Dunbar Ivy1, Steven H. Abman2, Robyn J. Barst3, Rolf M. F. Berger4, Damien Bonnet5, Thomas R. Fleming6, Sheila G. Haworth7, J. Usha Raj8, Erika B. Rosenzweig3, Ingram Schulze Neick7, Robin H. Steinhorn9, Maurice Beghetti10
1Colorado Children's Hospital, Pediatric Cardiology, University of Colorado School of Medicine, Aurora, Colorado, USA
2Colorado Children's Hospital, Pediatric Pulmonology, University of Colorado School of Medicine, Aurora, Colorado, USA
3Columbia University College of Physicians and Surgeons, New York, New York, USA
4Congenital Heart Disease Center, Pediatric Cardiology, Beatrix Children's Hospital, University of Groningen, Groningen University Medical Centre, Groningen, The Netherlands
5Necker Sick Children's Hospital, Centre de Référence malformations Cardiaques Congénitales Complexes (APHP) Pediatric Cardiology, Paris Descartes University, Paris, France
6Washington University, Department of Biostatistics, Seattle, Washington, USA
7Great Ormond Street Hospital, London, England
8Chicago Illinois University, Department of Pediatrics, Chicago, Illinois, USA
9University of California, Davis, Children's Hospital, Children's Clinic, Davis, California, USA
10University Hospital, Pediatric Cardiology Unit, Geneva, Switzerland

Pulmonary hypertension (PH) is a rare disease in newborns, infants, and children that is associated with significant morbidity and mortality. In the majority of pediatric patients, PH is idiopathic or associated with congenital heart disease and rarely is associated with other conditions such as connective tissue or thromboembolic disease. Incidence data from the Netherlands has revealed an annual incidence and point prevalence of 0.7 and 4.4 for idiopathic pulmonary arterial hypertension and 2.2 and 15.6 for pulmonary arterial hypertension, respectively, associated with congenital heart disease (CHD) cases per million children. The updated Nice classification for PH has been enhanced to include a greater depth of CHD and emphasizes persistent PH of the newborn and developmental lung diseases, such as bronchopulmonary dysplasia and congenital diaphragmatic hernia. The management of pediatric PH remains challenging because treatment decisions continue to depend largely on results from evidence based adult studies and the clinical experience of pediatric experts. (J Am Coll Cardiol 2013;62: D117–26) ©2013 by the American College of Cardiology Foundation.

Keywords: Congenital heart disease, pediatrics, pulmonary hypertension

How to cite this article
D. Dunbar Ivy, Steven H. Abman, Robyn J. Barst, Rolf M. F. Berger, Damien Bonnet, Thomas R. Fleming, Sheila G. Haworth, J. Usha Raj, Erika B. Rosenzweig, Ingram Schulze Neick, Robin H. Steinhorn, Maurice Beghetti. Pediatric pulmonary hypertension. Turk Kardiyol Dern Ars. 2014; 42(1): 153-164

Corresponding Author: D. Dunbar Ivy, United States
Manuscript Language: Turkish


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