ISSN 1016-5169 | E-ISSN 1308-4488
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A Williams-Beuren Syndrome with Critical Supravalvular Aortic Stenosis [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 1995; 23(4): 299-301

A Williams-Beuren Syndrome with Critical Supravalvular Aortic Stenosis

Y.Ergün ÇİL1, Y.Işık ŞENKAYA1, Mete CENGİZ1

A 4.5-year-old boy with the typical clinical aspects of Williams-Beuren syndrome who had severe supravalvular aortic stenosis was reported. Cardiac catheterization revealed 320 mmHg left ventricular systolic pressure and 180 mmHg supravalvular gradient. The stenosis was enlarged successfully with an oval-shaped patch by cardiopulmonary bypass technique. He was followed up for six months without any complication.

Keywords: Williams-Beuren syndrome, supravalvar aortic stenosis, cardiac catheterization

How to cite this article
Y.Ergün ÇİL, Y.Işık ŞENKAYA, Mete CENGİZ. A Williams-Beuren Syndrome with Critical Supravalvular Aortic Stenosis. Turk Kardiyol Dern Ars. 1995; 23(4): 299-301
Manuscript Language: Turkish


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