ISSN 1016-5169 | E-ISSN 1308-4488
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Marfan Syndrome: Surgical Management of Cardiovascular Complications [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 1994; 22(4): 261-264

Marfan Syndrome: Surgical Management of Cardiovascular Complications

Y.Suat BÜKET1, İsa DURMAZ1, Fatma AŞKAR1, Y.Alp ALAYUNT1, Y.Ahmet HAMULU1, Y.Mustafa ÖZBARAN1, Münevver YÜKSEL1, Kaya SÜZER1, İshak ARAS1, Tahir YAĞDI1, Yüksel ATAY1

Marfan syndrome's major manifestations involve the skeletal, ocular and cardiovascular systems. Multiple studies in patients with Marfan syndrome indicated that cardiovascular involvements may produce aneurysmal dilatation of the ascending aorta, aortic valvular regurgitation, aortic dissection, mitral valve prolapse and mitral regurgitation. These lesions are responsible for over 90% of deaths often in the third through fifth decades of life in patients with Marfan syndrome. In this paper 7 patients with Marfan syndrome, who underwent cardiovascular evaluation, were treated by combined composite valve graft replacement of the aortic root (5 patients), mechanical valve prosthesis replacement of the aortic valve and mitral valve replacement with mechanical valve prosthesis (one patient each). Patient follow-up ranged from 2 months to 4 years during which one patient died due to valve thrombosis 9 months postoperatively.

Keywords: Marfan syndrome, aortic ectasia annulo, aortic root dilatation

How to cite this article
Y.Suat BÜKET, İsa DURMAZ, Fatma AŞKAR, Y.Alp ALAYUNT, Y.Ahmet HAMULU, Y.Mustafa ÖZBARAN, Münevver YÜKSEL, Kaya SÜZER, İshak ARAS, Tahir YAĞDI, Yüksel ATAY. Marfan Syndrome: Surgical Management of Cardiovascular Complications. Turk Kardiyol Dern Ars. 1994; 22(4): 261-264
Manuscript Language: Turkish


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