ISSN 1016-5169 | E-ISSN 1308-4488
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A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation [Turk Kardiyol Dern Ars]
Turk Kardiyol Dern Ars. 2017; 45(6): 538-540 | DOI: 10.5543/tkda.2016.57262

A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation

Osman Güvenç1, Murat Saygı2, İbrahim Halil Demir3, Ender Ödemiş3
1Department of Pediatric Cardiology, Gynecologic and Pediatric Hospital, Batman, Turkey
2Department of Pediatric Cardiology, Gaziosmanpaşa Taksim Training and Research Hospital, İstanbul, Turkey
3Department of Pediatric Cardiology, Acıbadem University Faculty of Medicine, Istanbul, Turkey

Pulmonary arteriovenous malformation, which is defined as the presence of an ab-normal connection between the pulmonary artery and pulmonary vein, is rarely seen. Although it generally presents as a congenital condition, it may be accompanied by hereditary hemorrhagic telangiectasia. Clinical signs vary according to the amount of shunt in proportion to the number and size of the fistulae. Patients may present with cyanosis and respiratory trouble. If the disease remains untreated, it may result in cardiac failure and ineffective endocarditis, thereby leading to the rupture of the an-eurysmal fistula. Transcatheter embolization of abnormal vascular connection is the current treatment method in this disease. This article describes the case of an 8½-year-old child. He was presented with the symptom of getting tired quickly. Transcutaneous oxygen saturation of 75%, and pulmonary arteriovenous malfor-mation was detected in his examination. Successful transcatheter fistula embolization was performed.

Keywords: Child, fistula embolization, pulmonary arteriovenous malformation, cyanosis.

How to cite this article
Osman Güvenç, Murat Saygı, İbrahim Halil Demir, Ender Ödemiş. A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation. Turk Kardiyol Dern Ars. 2017; 45(6): 538-540

Corresponding Author: Osman Güvenç, Türkiye
Manuscript Language: Turkish


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